- HMDB0000491 (3-Methyl-2-oxovaleric acid)
- Cerebrospinal Fluid (CSF)
- Detected and Quantified
- Data source
- 101 uM
- Children (1-13 years old)
- Maple syrup urine disease
n=1. While patient was in coma.
- Wendel, U., Becker, K., Przyrembel, H. et al. (1980). Peritoneal dialysis in maple-syrup-urine disease: Studies on branched-chain amino and keto acids. Eur J Pediatr (1980) 134: 57. https://doi.org/10.1007/BF00442404. Eur J Pediatr.