Concentration Details

Metabolite
HMDB0000052 (Argininosuccinic acid)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
0 umol/mmol creatinine
Age
Adult (>18 years old)
Sex
Both
Condition
Normal
Comments
Not normally present in urine. Units are arbitrary.
References
    1. Erez A, Nagamani SC, Lee B: Argininosuccinate lyase deficiency-argininosuccinic aciduria and beyond. Am J Med Genet C Semin Med Genet. 2011 Feb 15;157C(1):45-53. doi: 10.1002/ajmg.c.30289. Epub 2011 Feb 10. [PubMed:21312326 ]