Concentration Details

Metabolite
HMDB0013128 (Valerylcarnitine)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
<0.310 uM
Age
Not Specified
Sex
Not Specified
Condition
Normal
References
    1. Sass JO, Ensenauer R, Roschinger W, Reich H, Steuerwald U, Schirrmacher O, Engel K, Haberle J, Andresen BS, Megarbane A, Lehnert W, Zschocke J: 2-Methylbutyryl-coenzyme A dehydrogenase deficiency: functional and molecular studies on a defect in isoleucine catabolism. Mol Genet Metab. 2008 Jan;93(1):30-5. doi: 10.1016/j.ymgme.2007.09.002. Epub 2007 Oct 22. [PubMed:17945527 ]