Concentration Details

Metabolite
HMDB0001067 (N-Acetylaspartylglutamic acid)
Biospecimen
Cerebrospinal Fluid (CSF)
Status
Detected and Quantified
Data source
Referenced
Concentration
18.7 (0.0-37.4) uM
Age
Adult (>18 years old)
Sex
Both
Condition
Canavan disease
References
    1. Burlina AP, Ferrari V, Divry P, Gradowska W, Jakobs C, Bennett MJ, Sewell AC, Dionisi-Vici C, Burlina AB: N-acetylaspartylglutamate in Canavan disease: an adverse effector? Eur J Pediatr. 1999 May;158(5):406-9. [PubMed:10333125 ]