- Metabolite
- HMDB0000716 (L-Pipecolic acid)
- Biospecimen
- Blood
- Status
- Detected and Quantified
- Data source
- Referenced
- Concentration
- 9.7 +/- 3.1 uM
- Age
- Adult (>18 years old)
- Sex
- Both
- Condition
- Zellweger syndrome
References
- Watkins PA, Chen WW, Harris CJ, Hoefler G, Hoefler S, Blake DC Jr, Balfe A, Kelley RI, Moser AB, Beard ME, et al.: Peroxisomal bifunctional enzyme deficiency. J Clin Invest. 1989 Mar;83(3):771-7. [PubMed:2921319 ]