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Identification
HMDB Protein ID HMDBP03124
Secondary Accession Numbers
  • 8668
Name Delta(3,5)-Delta(2,4)-dienoyl-CoA isomerase, mitochondrial
Synonyms Not Available
Gene Name ECH1
Protein Type Enzyme
Biological Properties
General Function Lipid transport and metabolism
Specific Function Isomerization of 3-trans,5-cis-dienoyl-CoA to 2-trans,4- trans-dienoyl-CoA
Pathways Not Available
Reactions Not Available
GO Classification
Function
catalytic activity
Process
metabolic process
Cellular Location
  1. Mitochondrion
  2. Peroxisome
Gene Properties
Chromosome Location Chromosome:1
Locus 19q13.1
SNPs ECH1
Gene Sequence
>987 bp
ATGGCGGCGGGGATAGTGGCTTCTCGCAGACTCCGCGACCTACTGACCCGGCGACTGACA
GGCTCCAACTACCCGGGACTCAGTATTAGCCTTCGCCTCACTGGCTCCTCTGCACAAGAG
GAGGCTTCCGGAGTAGCCCTCGGTGAAGCCCCAGACCACAGCTATGAGTCCCTTCGTGTG
ACGTCTGCGCAGAAACATGTTCTGCATGTCCAGCTCAACCGGCCCAACAAGAGGAATGCC
ATGAACAAGGTCTTCTGGAGAGAGATGGTAGAGTGCTTCAACAAGATTTCGAGAGACGCT
GACTGTCGGGCGGTGGTGATCTCTGGTGCAGGAAAAATGTTCACTGCAGGTATTGACCTG
ATGGACATGGCTTCGGACATCCTGCAGCCCAAAGGAGATGATGTGGCCCGGATCAGCTGG
TACCTCCGTGACATCATCACTCGATACCAGGAGACCTTCAACGTCATCGAGAGGTGCCCC
AAGCCCGTGATTGCTGCCGTCCATGGGGGCTGCATTGGCGGAGGTGTGGACCTTGTCACC
GCCTGTGACATCCGGTACTGTGCCCAGGATGCTTTCTTCCAGGTGAAGGAGGTGGACGTG
GGTTTGGCTGCCGATGTAGGAACACTGGAGCGCCTGCCCAAGGTCATCGGGAACCAGAGC
CTGGTCAACGAGCTGGCCTTCACCGCCCACAAGATGATGGCTGACGAGGCCCTGGACAGT
GGGCTGGTCAGCCGGGTGTTCCCAGACAAAGAGGTCATGCTGGATGCTGCCTTACCCCTG
GCGCCCGAGATTTCCAGCAAGACCACCGTGTTGGTGCAGAGCACCAAGGTCAACCTGCTG
TATTCCCGCGACCATTCGGTGGCCGAGAGCCTCAACTACGTGGCGTCCTGGAACATGAGC
ATGCTGCAGACCCAAGACCTCGTGAAGTCGGTCCAGCCCACGACTGAGAACAAGGAACTG
AAAACCGTCACCTTCTCCAAGCTCTGA
Protein Properties
Number of Residues 328
Molecular Weight 35815.8
Theoretical pI 8.12
Pfam Domain Function
Signals
  • None
Transmembrane Regions
  • None
Protein Sequence
>Delta(3,5)-Delta(2,4)-dienoyl-CoA isomerase, mitochondrial
MAAGIVASRRLRDLLTRRLTGSNYPGLSISLRLTGSSAQEEASGVALGEAPDHSYESLRV
TSAQKHVLHVQLNRPNKRNAMNKVFWREMVECFNKISRDADCRAVVISGAGKMFTAGIDL
MDMASDILQPKGDDVARISWYLRDIITRYQETFNVIERCPKPVIAAVHGGCIGGGVDLVT
ACDIRYCAQDAFFQVKEVDVGLAADVGTLQRLPKVIGNQSLVNELAFTARKMMADEALGS
GLVSRVFPDKEVMLDAALALAAEISSKSPVAVQSTKVNLLYSRDHSVAESLNYVASWNMS
MLQTQDLVKSVQATTENKELKTVTFSKL
GenBank ID Protein 2623168
UniProtKB/Swiss-Prot ID Q13011
UniProtKB/Swiss-Prot Entry Name ECH1_HUMAN
PDB IDs Not Available
GenBank Gene ID AF030249
GeneCard ID ECH1
GenAtlas ID Not Available
HGNC ID Not Available
References
General References
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  3. Choudhary C, Kumar C, Gnad F, Nielsen ML, Rehman M, Walther TC, Olsen JV, Mann M: Lysine acetylation targets protein complexes and co-regulates major cellular functions. Science. 2009 Aug 14;325(5942):834-40. doi: 10.1126/science.1175371. Epub 2009 Jul 16. [PubMed:19608861 ]
  4. Olsen JV, Blagoev B, Gnad F, Macek B, Kumar C, Mortensen P, Mann M: Global, in vivo, and site-specific phosphorylation dynamics in signaling networks. Cell. 2006 Nov 3;127(3):635-48. [PubMed:17081983 ]
  5. FitzPatrick DR, Germain-Lee E, Valle D: Isolation and characterization of rat and human cDNAs encoding a novel putative peroxisomal enoyl-CoA hydratase. Genomics. 1995 Jun 10;27(3):457-66. [PubMed:7558027 ]