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alpha-Ketoisovaleric acid+[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] lipoyllysine=[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine+CO(2)
Thumb+[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] lipoyllysine=[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine+CO(2)

Enzymes

  1. 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial

Status

    Experimental Data