Accession NumberHMDB00317
Common_Name2-Hydroxy-3-methylpentanoic acid
Description2-hydroxy-3-methylvaleric acid is an organic acid generated by L-isoleucine metabolism. It is found in the urine of normal individuals but in very elevated levels in patients with maple syrup urine disease (MSUD) (PMID 1429566). Maple syrup urine disease (MSUD) is an inherited metabolic disease predominantly characterized by neurological dysfunction including psychomotor/delay/mental retardation
Chemical_IUPAC_Name(2R,3R)-2-hydroxy-3-methyl-pentanoic acid
Chemical FormulaC6H12O3
Sample ConcentrationNot Available
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Predicted 1H NMR SpectrumDownload
Predicted 1H NMR PeaklistDownload
Predicted 13C NMR SpectrumDownload
Predicted 13C NMR PeaklistDownload
Sample ConcentrationNot Available
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1H NMR SpectrumNot Available
Sample ConcentrationNot Available
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ManufacturerNot Available
FrequencyNot Available
13C NMR SpectrumNot Available
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