Accession NumberHMDB06512
Common_Name3-mercaptolactate-cysteine disulfide
Description3-mercaptolactate-cysteine disulfide is a compound analog of cysteine excreted in the urine of patients affected by Mercaptolactate-cysteine disulfiduria (MCDU, OMIM 249650), the product of disorder of sulfur amino acid metabolism and a reduced activity of the enzyme mercaptopyruvate sulfurtransferase (MST, EC 2.8.1.2). Reduction of protein in the diet, addition of pyridoxine or of neomycin did not affect the urinary excretion of beta-mercaptolactate-cysteine disulfide of a mentally defective patient who was excreting this mixed disulfide. Addition of cysteine to the diet did increase the excretion of this disulfide (PMID: 3888441, 527218, 6945862, 5644041)
Chemical_IUPAC_Name(2R)-2-amino-3-(2,3-dihydroxy-3-oxopropyl)disulfanylpropanoic acid
Chemical FormulaC6H11NO5S2
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Predicted 1H NMR SpectrumDownload
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Predicted 13C NMR PeaklistDownload
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