Accession NumberHMDB01104
Common_NameN-Acetyl-b-glucosaminylamine
DescriptionN-Acetyl-b-glucosaminylamine is the product of a reaction catalyzed vy the enzyme N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase [EC 3.5.1.26, Aspartylglucosaminidase, AGA]. AGA is a key enzyme in the catabolism of N-linked oligosaccharides of glycoproteins. It cleaves the asparagine from the residual N-acetylglucosamines as one of the final steps in the lysosomal breakdown of glycoproteins. Aspartylglucosaminuria (AGU) is a lysosomal disease caused by deficiency of N-aspartyl-beta-glucosaminidase. AGU is the only known lysosomal storage disease caused by an amidase deficiency. (OMIM208400)
Chemical_IUPAC_Name2-acetamido-2-deoxy-beta-D-glucopyranosylamine
Chemical FormulaC8H16N2O5
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Predicted 13C NMR PeaklistDownload
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